【摘要】 目的 探讨肝豆状核变性患者视频脑电图改变。方法 对28例肝豆状核变性(HLD)患者及20例健康对照组视频脑电图监护检查。结果 发现HLD患者VEEG异常率达78.52%，明显高于健康对照组的异常率(20%)(P<0.01)，其VEEG异常主要表现为基本节律慢化，阵发性慢波和癫痫放电。结论 视频脑电图显著提高肝豆状核变性患者的脑电图检查的阳性率。脑电图的异常以基本律慢化为主，各型之间无特异性。脑电图检查可作为病情程度及疗效的观察指标之一。

    【关键词】 肝豆状核变性； 视频脑电图

    【Abstract】 Objective To discuss the VEEG changes in hepatolenticular degeneration patients.Methods VEEG was performed in 28 patients with hepatolenticular degeneration(HLD) and 20 control subjects.Results The abnormality rate of VEEG was 78.52% in the patient group, apparently higher than that of the control group (20%,P<0.01). The slowdown of the basic rhythm, paroxysmal slow wave and epileptiform discharges were the main changes in VEEG.Conclusion VEEG could obviously improve the abnormality rate of electroencephalogram in HLD patients. The abnormality rate of VEEG mainly were the slowdown of the basic rhythm. There no significance among the groups. VEEG could be regarded as one index of pathological degree and curative effect. ......